Description
Inclusion Criteria:
- * Diagnosis of group 1 Pulmonary Atrial Hypertension (PAH) diagnosed during right heart catheterization (RHC) according to WHO criteria 28
- * WHO functional class II to III
- * Stable clinical condition, with no change in medical therapy for pulmonary arterial hypertension (PAH) for at least 3 months before enrollment
- * Planned follow-up at University of Michigan Hospital Centers over at least 1 year
- * If enrolled in clinical trial, must be in open-label extension stage on stable medications for at least 3 months.
- * Competent to give informed consent
- * Have computer and internet access
Exclusion Criteria:
- * Life expectancy under 1 year
- * Co-morbidities which limit physical activity to a severe degree (i.e., permanently wheelchair bound, musculoskeletal disorders, recent myocardial infarction, unstable arrhythmia)
- * Current substance abuse, and/or a severe psychiatric disorder (including severe depression, psychosis, or dementia) which limits the patient's ability to follow the study protocol
- * Recently completed (\<6 months), current enrollment or planned enrollment in pulmonary rehab.
- * ≥30 minutes of exercise, ≥ 1 day per week for the previous 3 months
- * Six-minute walk distance \<150 meters or \>550 meters
- * Moderate or severe obstructive lung disease forced expiratory volume/forced vital capacity (FEV1/FVC) \< 70% and FEV1 \< 65% of predicted value after bronchodilator administration).
- * Moderate or severe restrictive lung disease (total lung capacity \< 60% predicted value).
- * Arterial oxygen saturation (SpO2) \<88% during 6-minute walk test on baseline home oxygen prescription if applicable or SpO2 \<80% if uncorrected shunt.
- * History of exercise-induced syncope or arrhythmias.
- * Pregnancy or lactation
- * Non-English speaking
Ages Eligible for Study:
18 Years to N/A (ADULT, OLDER_ADULT)
Sexes Eligible for Study: ALL
Accepts Healthy Volunteers:
No